Physician
Rheumatology
Dr. Paul H. Plotz, MD
Paul Plotz is an expert in the field of Rheumatology. He received awards:"Elected Member". Paul Plotz has written publications. He has 25 publications published with PubMed. The lastest paper is: 'Autoimmunity: the history of an idea.'
Publications
- Autoimmunity: the history of an idea.
- The hygiene hypothesis.
- Differences in the predominance of lysosomal and autophagic pathologies between infants and adults with Pompe disease: implications for therapy.
- Suppression of autophagy permits successful enzyme replacement therapy in a lysosomal storage disorder--murine Pompe disease.
- Validation of manual muscle testing and a subset of eight muscles for adult and juvenile idiopathic inflammatory myopathies.
- Fiber type conversion by PGC-1α activates lysosomal and autophagosomal biogenesis in both unaffected and Pompe skeletal muscle.
- The values and limits of an in vitro model of Pompe disease: the best laid schemes o' mice an' men...
- Murine muscle cell models for Pompe disease and their use in studying therapeutic approaches.
- Distribution and severity of weakness among patients with polymyositis, dermatomyositis and juvenile dermatomyositis.
- Deconstructing Pompe disease by analyzing single muscle fibers: to see a world in a grain of sand...
- Acid alpha-glucosidase deficiency (Pompe disease).
- Autophagy and mistargeting of therapeutic enzyme in skeletal muscle in Pompe disease.
- Autophagy and lysosomes in Pompe disease.
- Dysfunction of endocytic and autophagic pathways in a lysosomal storage disease.
- Immunogenetic risk and protective factors for the idiopathic inflammatory myopathies: distinct HLA-A, -B, -Cw, -DRB1, and -DQA1 allelic profiles distinguish European A...
- Immunogenetic risk and protective factors for the idiopathic inflammatory myopathies: distinct HLA-A, -B, -Cw, -DRB1 and -DQA1 allelic profiles and motifs define clini...
- Seasonal influence on the onset of idiopathic inflammatory myopathies in serologically defined groups.
- Replacing acid alpha-glucosidase in Pompe disease: recombinant and transgenic enzymes are equipotent, but neither completely clears glycogen from type II muscle fibers.
- Myositis: an update on pathogenesis.
- Glycogen stored in skeletal but not in cardiac muscle in acid alpha-glucosidase mutant (Pompe) mice is highly resistant to transgene-encoded human enzyme.
- Animal models of myositis.
- Histidyl-tRNA synthetase and asparaginyl-tRNA synthetase, autoantigens in myositis, activate chemokine receptors on T lymphocytes and immature dendritic cells.
- Correction of the enzymatic and functional deficits in a model of Pompe disease using adeno-associated virus vectors.
- Hes-1, a known transcriptional repressor, acts as a transcriptional activator for the human acid alpha-glucosidase gene in human fibroblast cells.
Schools
Harvard Medical School
Doctors Specialties
- Internal Medicine
- Rheumatology
Accepted Insurances
Awards
- Elected Member
Education
-
Beth Israel Deaconess Medical Center
Helpful Reviews
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